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Peripheral T-cell lymphoma, not classified, extranodal and solid organ sites

ICD10CM code

Name of the Condition

  • Peripheral T-cell lymphoma, not elsewhere classified, extranodal and solid organ sites (ICD-10 Code: C84.49)

Summary

  • Peripheral T-cell lymphoma, not elsewhere classified, is a rare, aggressive form of non-Hodgkin lymphoma. It originates from mature T-cells and primarily affects organs other than the lymph nodes, such as the liver, spleen, or skin.

Causes

  • The exact cause is unclear, but genetic mutations, immune system deficiencies, and viral infections like the Epstein-Barr virus (EBV) may contribute to its development.

Risk Factors

  • Risk factors include older age, male gender, a history of autoimmune diseases, exposure to certain chemicals, and infections with viruses like HTLV-1 or EBV.

Symptoms

  • Symptoms may include swelling or lumps, fatigue, fever, night sweats, unexplained weight loss, and organ-related symptoms depending on where the lymphoma has spread.

Diagnosis

  • Diagnosis typically involves a combination of physical examination, imaging tests (e.g., CT or PET scans), blood tests, and biopsy of affected tissues for histological analysis.

Treatment Options

  • Treatment may involve chemotherapy, radiation therapy, or a combination of both. Stem cell transplant might be considered in certain cases. Treatments aim to eliminate cancer cells and manage symptoms.

Prognosis and Follow-Up

  • The prognosis varies based on factors like the stage at diagnosis and response to treatment. Regular follow-ups are crucial to monitor for recurrence and manage potential side effects of treatment.

Complications

  • Potential complications include infection, organ failure, and treatment-related side effects, such as fatigue and susceptibility to further health issues.

Lifestyle & Prevention

  • While specific prevention strategies are limited due to the unclear causes, maintaining a healthy lifestyle with a balanced diet and regular exercise can support overall health and immune function.

When to Seek Professional Help

  • Seek medical attention for persistent and unexplained symptoms such as lumps, extreme fatigue, or significant weight loss to rule out serious conditions like lymphoma.

Additional Resources

  • Leukemia & Lymphoma Society (LLS)
  • Lymphoma Research Foundation (LRF)

Tips for Medical Coders

  • Verify the site of the lymphoma to ensure correct coding; extranodal and solid organ sites should be distinguished from lymph node involvement.
  • Avoid errors by confirming that the classification is "not elsewhere classified" under peripheral T-cell lymphoma.

Medical Policies and Guidelines for Peripheral T-cell lymphoma, not classified, extranodal and solid organ sites

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