Q87.418 Marfan's syndrome with other cardiovascular manifestations

ICD-10-CM Q87.418: Marfan's syndrome with other cardiovascular manifestations

ICD-10-CM code Q87.418 identifies Marfan's syndrome with cardiovascular manifestations other than aortic dilation. Marfan syndrome is an inherited connective tissue disorder affecting multiple body systems, including the cardiovascular system. This code is distinct from related codes specifying aortic dilation, ocular, or skeletal manifestations. The provided sources establish the code's existence and clinical context but do not address coverage. 1 3 5 6

Plain-language overview

Marfan syndrome is an inherited disorder of connective tissue that affects multiple body systems, including the cardiovascular, musculoskeletal, and ocular systems. Clinical manifestations may be apparent in infancy, or affected individuals may present later in adolescence or young adulthood. 6

Clinical context

Marfan syndrome is an autosomal dominant condition with a reported incidence of 1 in 3000 to 5000 individuals. The syndrome is associated with classic ocular, cardiovascular, and musculoskeletal abnormalities, and decreased life expectancy occurs primarily due to aortic complications. 1

What this code represents

ICD-10-CM diagnosis code Q87.418 represents Marfan's syndrome with other cardiovascular manifestations. This specific code is listed alongside Q87.410 for Marfan's syndrome with aortic dilation and Q87.40 for Marfan's syndrome unspecified. 3 5

Coding details

The broader category Q87.41 denotes Marfan's syndrome with cardiovascular manifestations. Within this category, Q87.418 is distinguished from Q87.410, which is specifically designated for Marfan's syndrome with aortic dilation. 3

Additional codes in this classification include Q87.42 for Marfan's syndrome with ocular manifestations and Q87.43 for Marfan's syndrome with skeletal manifestation. These codes allow for the specification of different body systems affected by the syndrome. 3 5

Documentation considerations

The provided code lists identify Q87.418 as a distinct diagnosis from Q87.410, which is used for aortic dilation. Selecting Q87.418 indicates the documentation supports a cardiovascular manifestation of Marfan's syndrome other than aortic dilation. 3 5

What the sources add

The clinical reference sources describe Marfan syndrome as an inherited disorder affecting connective tissue and multiple organ systems. In contrast, the code list sources provide the specific ICD-10-CM numerical codes used to classify these distinct cardiovascular and skeletal manifestations. 1 3 6

One code list source includes Q87.418 within a broader document of ICD-10 codes for visible congenital deformities. Another code list source identifies Q87.418 as an ICD-10-CM diagnosis within a compilation of congenital cardiac malformations. 3 5

Coverage and utilization context

The provided sources establish the clinical description of Marfan syndrome and the formal ICD-10-CM code titles. None of the supplied excerpts contain information regarding payer-specific coverage, reimbursement policies, or utilization management rules for code Q87.418. 1 3 5 6

Sources

1. Bookshelf — ncbi.nlm.nih.gov; accessed 2026-07-25.
2. Bookshelf — ncbi.nlm.nih.gov; accessed 2026-07-25.
3. ICD 10 codes for reportable Visible Congenital Deformities — hhs.nd.gov; accessed 2026-07-25.
4. Phecode 758 · Cancer PRSweb — csg.sph.umich.edu; accessed 2026-07-25.
5. Disclaimer — sentinelinitiative.org; accessed 2026-07-25.
6. Marfan Syndrome | 5-Minute Clinical Consult — unboundmedicine.com; accessed 2026-07-25.