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Pompe disease

ICD10CM code

Medical Policies and Guidelines for Pompe disease

Related policies from health plans

Electrodiagnostic Testing (EMG/NCV) - (CPG129)
Pompe Disease [Lumizyme (alglucosidase alfa), Nexviazyme (avalglucosidase alfa-ngpt)]

Similar Codes


ICD10CM codes

E74.02 - Pompe disease
E74.03 - Cori disease
L30.1 - Dyshidrosis [pompholyx]
E83.3 - Disorders of phosphorus metabolism and phosphatases
K76.81 - Hepatopulmonary syndrome
E83.30 - Disorder of phosphorus metabolism, unspecified
E74.04 - McArdle disease
E70.331 - Hermansky-Pudlak syndrome
I27.82 - Chronic pulmonary embolism
I42 - Cardiomyopathy

HCPCS codes

C8957 - Intravenous infusion for therapy/diagnosis; initiation of prolonged infusion (more than 8 hours), re
E0784 - External ambulatory infusion pump, insulin
G8923 - Left ventricular ejection fraction (lvef) < 40% or documentation of moderately or severely depressed
E0675 - Pneumatic compression device, high pressure, rapid inflation/deflation cycle, for arterial insuffici
G8082 - End stage renal disease patient requiring hemodialysis documented to have received vascular access o
S9328 - Home infusion therapy, implanted pump pain management infusion; administrative services, professiona
G8934 - Left ventricular ejection fraction (lvef) <40% or documentation of moderately or severely depressed
G8947 - One or more neuropsychiatric symptoms
G9842 - Patient has metastatic disease at diagnosis
E0454 - PRESSURE VENTILATOR

CPT4 codes

33676 - Closure of multiple ventricular septal defects; with pulmonary valvotomy or infundibular resection (
83986 - pH; body fluid, not otherwise specified
33979 - Insertion of ventricular assist device, implantable intracorporeal, single ventricle
33975 - Insertion of ventricular assist device; extracorporeal, single ventricle
33675 - Closure of multiple ventricular septal defects
33953 - Extracorporeal membrane oxygenation (ECMO)/extracorporeal life support (ECLS) provided by physician;
33976 - Insertion of ventricular assist device; extracorporeal, biventricular
81330 - SMPD1(sphingomyelin phosphodiesterase 1, acid lysosomal) (eg, Niemann-Pick disease, Type A) gene ana
91299 - Unlisted diagnostic gastroenterology procedure
62200 - Ventriculocisternostomy, third ventricle