Search all medical codes
Sjogren syndrome with keratoconjunctivitis
ICD10CM code
Name of the Condition
- Sjogren Syndrome with Keratoconjunctivitis
- Also known as: Sjogren's Syndrome with dry eyes, Autoimmune exocrinopathy.
Summary
- Sjogren syndrome with keratoconjunctivitis is an autoimmune disorder where the body's immune system mistakenly attacks its moisture-producing glands, leading to dryness, particularly in the eyes, mouth, and other organs. Keratoconjunctivitis refers specifically to the inflammation and dryness affecting the cornea and conjunctiva of the eyes.
Causes
- The exact cause is unknown but is believed to involve a combination of genetic, environmental, and possibly viral triggers. The body's immune response mistakenly targets the glands, reducing their ability to produce moisture.
Risk Factors
- More common in women than men.
- Typically occurs in individuals aged 40 and above.
- Family history of autoimmune diseases.
- Presence of another autoimmune disease, such as rheumatoid arthritis or lupus.
Symptoms
- Persistent dry eyes and mouth.
- Redness and irritation of the eyes.
- Sensation of sand or grit in the eyes.
- Difficulty swallowing or speaking due to mouth dryness.
- Fatigue and joint pain in some cases.
Diagnosis
- Blood tests to check for specific antibodies.
- Schirmer's test to measure tear production.
- Eye examination with a slit lamp.
- Salivary gland function tests or biopsy.
Treatment Options
- Artificial tears and eye lubricants to relieve eye dryness.
- Immunosuppressive drugs like hydroxychloroquine or corticosteroids for severe cases.
- Saliva substitutes or medications like pilocarpine to stimulate salivary gland function.
- Lifestyle adaptations to manage symptoms, such as using a humidifier or avoiding caffeine.
Prognosis and Follow-Up
- While there is no cure, symptoms can often be effectively managed with treatment.
- Regular follow-up and monitoring are essential to manage symptoms and adjust treatments as needed.
Complications
- Increased risk of eye infections due to severe dryness.
- Dental issues, such as cavities, due to reduced saliva.
- Potential development of other autoimmune conditions.
Lifestyle & Prevention
- Stay hydrated by drinking plenty of water.
- Use a humidifier to maintain indoor humidity.
- Avoid smoking and exposure to dry, windy environments.
- Regular dental check-ups to prevent oral complications.
When to Seek Professional Help
- Severe or persistent dry eyes or mouth.
- Sudden changes in vision or eye pain.
- Difficulty swallowing or new onset of joint pain.
Additional Resources
Tips for Medical Coders
- Ensure to differentiate primary Sjogren's syndrome from secondary forms when coding.
- Watch for related symptoms or conditions in patient's medical history that could impact coding accuracy.
- Verify lab results and doctor notes to correctly code for keratoconjunctivitis involvement.