Name of the Procedure:

Special Enteral Formula for Pediatrics with Metabolic Needs Technical term: B4162 – Enteral formula for pediatrics, special metabolic needs for inherited disease of metabolism

Summary

In this procedure, a specially formulated liquid nutrition designed for children with inherited metabolic disorders is provided through an enteral feeding tube. This formula includes all essential nutrients—proteins, fats, carbohydrates, vitamins, and minerals—and may include fiber, delivering 100 calories per unit.

Purpose

This specialized enteral formula aims to meet the unique nutritional needs of children with inherited metabolic disorders. It ensures they receive the vital nutrients necessary for growth and development while managing their specific metabolic requirements.

Indications

• Children diagnosed with inherited diseases of metabolism
• Inadequate oral intake of nutrients
• Specific dietary needs that can't be met through standard nutrition

Preparation

• No specific patient preparation is required.
• Prior assessment by a healthcare professional to determine nutritional needs.
• Possible adjustments in existing medications or diet based on individual conditions.

Procedure Description

1. Assessment: A healthcare professional evaluates the child's nutritional and metabolic needs.
2. Selection: The appropriate enteral formula is chosen based on the assessment.
3. Setup: An enteral feeding tube is inserted if not already in place.
4. Administration: The specialized formula is administered through the feeding tube, typically using a pump or gravity drip.
5. Monitoring: Continuous monitoring to ensure proper absorption and tolerance.

Duration

• Initial setup and feeding may take approximately 30 minutes to 1 hour.
• Ongoing feeding duration depends on the individual schedule set by the healthcare team.

Setting

• Hospital
• Outpatient clinic
• Home, under supervision or with trained caregivers

Personnel

• Pediatrician or specialist in metabolic disorders
• Registered dietitian
• Nurses or trained caregivers

Risks and Complications

• Tube dislodgement or blockage
• Infection at the tube insertion site
• Gastrointestinal discomfort or intolerance
• Nutrient imbalances if not properly monitored

Benefits

• Tailored to meet the unique nutritional needs of children with inherited metabolic disorders
• Supports growth and development
• May help manage metabolic disturbances and prevent complications related to nutrient deficiencies

Recovery

• Continuous feeding as per prescribed schedule
• Regular follow-up appointments to monitor nutritional status and adjust the formula if necessary
• Care for the feeding tube site to prevent infections

Alternatives

• Oral special metabolic formulas, which may not be feasible for all patients
• Parenteral nutrition (intravenous), typically more invasive and for severe cases
• The pros of enteral formula include less invasiveness and closer mimicry of natural feeding, while alternatives might be necessary in more critical conditions.

Patient Experience

• Initial discomfort or adjustment period with the feeding tube
• Close interaction with healthcare providers for monitoring and adjustments
• Pain management and comfort measures typically manage any discomfort experienced during and after the introduction of the feeding tube.